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Resection of a functioning intrapericardial paraganglioma associated with succinate dehydrogenase B mutation
journal contribution
posted on 2023-05-22, 03:52 authored by Siejka, DA, Vittorio, AF, Thakur, S, John BurgessJohn Burgess, Harkikar, AFunctional paragangliomas are rare neuroendocrine tumours that secrete catecholamines and are infrequently found in the mediastinum. We report a case of a young male with symptoms of catecholamine excess and a personal and family history of the paraganglioma predisposing succinate dehydrogenase subunit B mutation. The lesion had anatomical intrapericardial juxtaposition to important cardiac anatomy and posed the significant challenge of dissection at surgery. The lesion was successfully resected via sternotomy on cardiopulmonary bypass and confirmed histopathologically as paraganglioma. Intrapericardial paraganglioma is rare and treatment is difficult and time critical considering the proximity of cardiac anatomy as well as malignant potential.
History
Publication title
SAGE open medical case reportsISSN
2050-313XDepartment/School
Tasmanian School of MedicinePublisher
SAGE PublicationsPlace of publication
United KingdomRepository Status
- Restricted